一种实验室和临床指标酷似血友病甲的新的变异型血管性假血友病最近被发现。以往,它一直被误诊为血友病甲.本综述旨在总结其表型和基因型特征、探讨鉴别和研究该变异型的理论意义和医学价值。 A new variant of vasculogenic hemophilia resembling hemophilia A, a laboratory and clinical indicator, was recently discovered. In the past, it has been misdiagnosed as hemophilia A. The purpose of this review is to summarize its phenotype and genotype characteristics and to explore the theoretical and medical implications of identifying and studying this variant.