致心律失常性右室心肌病(ARVC),又称致心律失常性右室发育不良/心肌病(ARVD/C),目前已经明确其是一种遗传性疾病,至少50%的病例表现为典型的常染色体显性遗传,也有常染色体隐性遗传的报道。2006年新颁布的心肌病分类将ARVC归属于遗传性原发性心肌病。根据临床研究和参加体育运动前的筛查资料,估计ARVC在一般人群的患病率为1/1 000～1/5 000。发病年龄80%在40岁之前,男性占 Arrhythmogenic right ventricular cardiomyopathy (ARVC), also known as arrhythmogenic right ventricular dysplasia / cardiomyopathy (ARVD / C), has now been identified as a hereditary disease with at least 50% of cases presenting as typical Autosomal dominant inheritance, there are also reports of autosomal recessive inheritance. The new 2006 cardiomyopathy classification ARVC belongs to hereditary primary cardiomyopathy. Based on clinical studies and pre-sport screening data, the prevalence of ARVC in the general population is estimated to be 1/1 000 to 1 in 5000. Age 80% of onset before the age of 40, accounted for by men