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阵发性睡眠性血红蛋白床症（PNH）是后大性基因缺陷引起的一种溶血病，由于其变异起始发生在造血干细胞水平，所以外周血细胞都随之有变化，病态血细胞膜的共同特点是细胞膜缺乏含有糖肌酸磷脂结合蛋白（简称GPI一蛋白）、这类蛋白大约有80多忡．分布很广，在血细胞上有十几种
Paroxysmal nocturnal hemoglobin disease (PNH) is a hemolytic disease caused by a large genetic defect, and as its variation begins at the level of hematopoietic stem cells, peripheral blood cells change, and the common features of diseased blood cell membranes Is a lack of cell membrane containing glycosylated phospholipid binding protein (GPI a protein for short), about 80 kinds of such proteins. Distribution is very wide, there are dozens of blood cells