间叶性软骨肉瘤发生在骨外者罕见。国外1980年以前仅有30余例报道,国内报告更少。现将我院见到的1例发生在颅内的原发性间胚叶性软骨肉瘤报告如下: 患者,女性、19岁,因头痛半年,双眼肿胀伴视力下降1月余,于1986年3月17日入院。检查:神志清楚,双侧瞳孔等大,对光反射存在,眼底水肿,左眼外展差,无面瘫、伸舌居中,四肢肌张力正常,腱 Mesenchymal chondrosarcoma in the bone are rare. Only 30 cases were reported abroad before 1980, with fewer domestic reports. Now in our hospital to see a case occurred in the intracranial primary mesenchymal embryonal chondrosarcoma are reported as follows: patients, women, 19 years old, due to headache for six months, both eyes with decreased visual acuity more than 1 month in 1986, 3 January 17 admission. Check: conscious, bilateral pupils and other large, the presence of light reflex, fundus edema, poor left eye abduction, no facial paralysis, extensor middle limb, limb muscle tone normal, tendon