血管外皮瘤是起源于血管外皮细胞的肿瘤,多发于全身软组织,原发于骨骼罕见。骨的血管外皮瘤多因发病部位持续性疼痛或剧痛来诊。病程约3～6个月,常合并功能障碍或病理性骨折。诊断取决于病理,易误诊。肿瘤行外科广泛切除,术前选择性动脉栓塞,术后继续放疗和化疗是比较合适的治疗方法。作者报告6例并结合文献对此瘤的患病率、病理分类、临床表现、X 线表现和治疗等进行讨论。 Hemangiopericytomas are tumors that originate in the vascular skin cells and occur in the soft tissues of the body. They are rare in the bones. Hemangiocutaneous tumors of the bone often have persistent pain or severe pain at the site of the disease. Duration of about 3 to 6 months, often with functional disorders or pathological fractures. The diagnosis depends on the pathology and is often misdiagnosed. Extensive surgical resection of the tumor, selective arterial embolization before surgery, continued radiotherapy and chemotherapy after surgery is a more appropriate treatment. The authors reported 6 cases and combined the literature to discuss the prevalence, pathological classification, clinical manifestations, X-ray findings and treatment of the tumor.