限制性心肌病的临床征象和血流动力学表现,酷似缩窄性心包炎,而常难以相互鉴别。多数限制性心肌病的病理基础具有心肌浸润性病变。本文报道4例限制性心肌病患者的临床、血流动力学及形态学资料并不具有常见的病理学基础。病人与方法:4例患者年龄59～77岁(平均66岁)。(1)临床表现 4例均有呼吸困难,下肢浮肿或腹水等双心室衰竭症状已4～8年。1例早在出现充血性心力衰竭症状之前已有完全性房室传导阻滞14年。1例在13年前已发现房性心律失常。另1例有 The clinical signs and hemodynamic manifestations of restrictive cardiomyopathy resemble constrictive pericarditis and are often difficult to identify with each other. The pathological basis of most restrictive cardiomyopathy has myocardial infiltrates. This article reports 4 patients with restrictive cardiomyopathy clinical, hemodynamic and morphological data does not have a common pathological basis. Patients and Methods: Four patients aged 59-77 years (mean, 66 years). (1) 4 cases of clinical manifestations have dyspnea, lower extremity edema or ascites and other symptoms of biventricular failure has been 4 to 8 years. One patient had complete atrioventricular block for 14 years prior to the onset of symptoms of congestive heart failure. One patient had atrial arrhythmia 13 years ago. Another case there