原发性骨髓纤维化症是骨髓增殖性疾病之一。本病具有贫血、肝脾肿大、未稍血象出现幼稚粒细胞和有核红细胞以及不同程度的骨髓纤维化表现。本病的名称颇多,如骨髓硬化、组织髓样化生,具有髓样化生的骨髓硬化症、原因不明性的髓外化生、原因不明性的髓外造血等40余种。国内报告甚少,我们在病房曾收治一例,现报告如下。患者刘×,男、60岁、工人。病人20年前曾因左上腹胀闷不适,消化不良而在某医院就诊,诊断为“班替氏综合征”、未予特 Primary myelofibrosis is one of myeloproliferative diseases. The disease has anemia, hepatosplenomegaly, not a little blood like juvenile granulocytes and nucleated erythrocytes and varying degrees of myelofibrosis performance. The name of the disease quite a lot, such as bone marrow sclerosis, myeloid metaplasia, myeloid metaplasia with myeloid metaplasia, unexplained extramedullary metaplasia, extramedullary hematopoiesis of unknown reason more than 40 species. There are very few domestic reports. One case was admitted to the ward and the report is as follows. Patient Liu ×, male, 60 years old, worker. 20 years ago, the patient had a left upper quadruple abdominal distention discomfort, indigestion and treatment at a hospital, diagnosed as “Bentell’s syndrome,” no special