Wagner于1863年首次报告原发性炎症性肌肉疾病。本病的特点是横纹肌的弥漫性炎症,主要引起对称性进行性近端肌肉软弱乏力和肌肉萎缩。1891年Umverrich报告了同样疾病,因其特征为伴有皮损,故命名为皮肌炎。 皮肌炎在在临床上并非罕见,现结合我院14例皮肌炎患者的临床资料和有关文献进行讨 Wagner first reported primary inflammatory muscle disease in 1863. The disease is characterized by diffuse striated striated inflammation, mainly caused by the symmetry of proximal muscle weakness and muscle atrophy. 1891 Umverrich reported the same disease, because of its associated with skin lesions, so named dermatomyositis. Dermatomyositis is not uncommon in clinical practice, now combined with the clinical data of 14 patients with dermatomyositis in our hospital and related literature