论文部分内容阅读
视网膜色素变性(Retinitis pigmentosa,简称RP)是一组进行性遗传性眼病.广泛地损害感光细胞和色素上皮功能。临床上以暗适应下降.周边视野逐渐向心性缩窄,视力日渐减退为特点,并伴有特征性的眼底异常。随着科学的不断进步,许多致盲性眼病已得到不同程度的控制,而RP的致盲率则有所上升。RP的发病在世界各国不一。有资料报告:全世界如按40亿人口计,RP病人约有两千万人(5‰);在中国的发病率为1/4000,英国为1/4900,美国为1/5200,瑞士为1/7000,以色列为1/4500,在日本则为1/9000。本病的确切病因及发病机理尚无定论。目前认为该病
Retinitis pigmentosa (RP) is a group of progressive hereditary eye diseases that extensively impair photoreceptor cell and pigment epithelial function. Clinically, dark adaptation decreased peripheral vision gradually narrowed to the heart, visual acuity diminished as characterized by, and associated with characteristic fundus abnormalities. With the continuous progress of science, many blinding eye diseases have been controlled to some extent, while the blinding rate of RP has increased. The incidence of RP varies in different countries in the world. According to the data report, there are about 20 million RP patients (5 ‰) in the world, with a population of 4 billion. The incidence in China is 1/4000, that in the United Kingdom is 1/4900, that in the United States is 1/5200, and that in Switzerland is 1/7000 for Israel, 1/4500 for Israel and 1/9000 for Japan. The exact etiology and pathogenesis of this disease is inconclusive. The disease is currently considered