门静脉海绵样变性（CavernousTransformationofthePortalVein）是一种因门静脉先天性海绵样畸变导致门静脉主干完全或部分闭塞而致的肝外型门静脉高压症，临床罕见。现将我们应用脾脏分流术治疗此病的临床体会结合文献报告如下。1临床病例病人，男，6岁，因反复少量呕血黑便在 Portal venous cavernous degeneration (Cavernous Transformation of the Portalal Vein) is a due to portal vein congenital cavernous distortion leading to complete or partial obstruction of the main portal vein due to extrahepatic portal hypertension, clinically rare. Now we apply spleen shunt surgery for the clinical experience combined with the literature report is as follows. A clinical case of patients, male, 6 years old, due to repeated small hematemesis in vomiting