Primary cardiac tumors are extremely rare with occurrence range of about 0.0017-0.28%.Papillary fibroelastoma is one of such benign cardiac neoplasms.Improvement in the early diagnosis has been made possible with the help of high-resolution imaging technology,such as transesophageal echocardiography,combined with ischemic or embolic complications which patients typically present with clinically.We herein present a 51-year-old female patient with a papillary fibroelastoma on the aortic cusp,with its origin from the left coronary sinus.Her only clinical manifestation was angina-like chest pain and syncope.Surgical resection with aortic valve replacement due to the defect as a result of the resected tumor was performed with the patient on cardiopulmonary bypass.The patient recovered uneventfully and was discharged.A 2-year follow-up showed intact valve without tumor recurrence.