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Outline· Typical anti-GBM disease· Serologic testing for anti-GBM antibodies· "Atypical" anti-GBM disease Anti-GBM disease· Circulating antibodies against an antigen in the GBM· Clinical:· Acute kidney injury, hematuria, proteinuria· Pulmonary hemorrhage in 30-50%· Anti-GBM antibody production & disease is short-lived